The Air within A Case Report : Lymphangioleiomyomatosis (Record no. 8269)
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fixed length control field | 02596nam a22002057a 4500 |
003 - CONTROL NUMBER IDENTIFIER | |
control field | PILC |
005 - DATE AND TIME OF LATEST TRANSACTION | |
control field | 20240720152623.0 |
008 - FIXED-LENGTH DATA ELEMENTS--GENERAL INFORMATION | |
fixed length control field | 160505b2015 xxu||||| |||| 00| 0 eng d |
040 ## - CATALOGING SOURCE | |
Transcribing agency | FEU-NRMF MEDICAL LIBRARY |
041 ## - LANGUAGE CODE | |
Language code of text/sound track or separate title | English |
050 ## - LIBRARY OF CONGRESS CALL NUMBER | |
Classification number | RESRAD20150002 |
245 ## - TITLE STATEMENT | |
Title | The Air within A Case Report : Lymphangioleiomyomatosis |
260 ## - PUBLICATION, DISTRIBUTION, ETC. (IMPRINT) | |
Place of publication, distribution, etc. | QUEZON CITY |
Name of publisher, distributor, etc. | FEU-NRMF |
Date of publication, distribution, etc. | 2015 |
300 ## - PHYSICAL DESCRIPTION | |
Extent | 23 PAGES |
520 ## - SUMMARY, ETC. | |
Summary, etc. | ABSTRACT: Lymphangiomyomatosis (LAM) is a multi-systemic, rare, progressive and life threatening cystic lung disease that is predominantly sporadic and effects women of childbearing age. It is usually characterized by proliferation of atypical smooth muscle cells around lymphatics, venules and bronchioles. Generally, patient would present with respiratory symptoms varying from simple cough, chest pain, and dyspnea to recurrent pneumothorax as well as pleural effusion. Pneumothorax is almost always present in 50% of the case. Early stages may show normal findings radiographically, but this may progress from retriculo-nodular to cystic of the lung. LAM can often be confused with other disease entities such as bronchiectasis, emphysema, pulmonary Langerhan`s cell histiocytosis (LCH), lymphocytic interstitial pneumonitis and Birt Hogg Dube syndrome (BHD). Because of the similarities of the early signs and symptoms of LAM to other cystic lung disease, diagnostics such as radiography, computed tomography and pulmonary function test are commonly requested to aid in the diagnosis of LAM. This is a case of a 46-year old female who presented with difficulty of breathing and recurrent pneumothorax. Chest radiograph was done revealing repeated collapse of lungs. Likewise chest CT scan showed findings suggestive of Lymphangioleiomyomatosis. However, histopatologic tissue characterization (lung biopsy) remains the definite examination for the diagnosis of this rare disease, which in our patient revealed emphysematous changes with bronchiolectasis. Pulmonary lymphangioleiomyomatosis is progressive and worsens over time. Currently, there has been no cure available to stop the growth and progression of the cysts in LAM. Treatment goal is to ease symptoms and prevent further complication usually by giving medications to improve air flow of lungs, oxygen therapy, remove fluids through chest tubes and aspirations and lung transplantation for severe LAM. There are clinical trials and researches being done to discover and test new treatments for LAM. |
521 ## - TARGET AUDIENCE NOTE | |
Target audience note | Research |
700 ## - ADDED ENTRY--PERSONAL NAME | |
Personal name | Limpalan Tammang, Jovayna., M.D. |
887 ## - NON-MARC INFORMATION FIELD | |
Content of non-MARC field | RC RC 0019 |
942 ## - ADDED ENTRY ELEMENTS (KOHA) | |
Source of classification or shelving scheme | Library of Congress Classification |
Koha item type | Research |
Withdrawn status | Lost status | Source of classification or shelving scheme | Damaged status | Not for loan | Home library | Current library | Shelving location | Date acquired | Total Checkouts | Full call number | Barcode | Date last seen | Price effective from | Koha item type |
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Library of Congress Classification | Far Eastern University - Nicanor Reyes Medical Foundation | Far Eastern University - Nicanor Reyes Medical Foundation | Research | 01/18/2016 | RAD20150002 | R000465 | 03/01/2016 | 07/22/2016 | Research |