The Air within A Case Report : Lymphangioleiomyomatosis (Record no. 8269)

MARC details
000 -LEADER
fixed length control field 02596nam a22002057a 4500
003 - CONTROL NUMBER IDENTIFIER
control field PILC
005 - DATE AND TIME OF LATEST TRANSACTION
control field 20240720152623.0
008 - FIXED-LENGTH DATA ELEMENTS--GENERAL INFORMATION
fixed length control field 160505b2015 xxu||||| |||| 00| 0 eng d
040 ## - CATALOGING SOURCE
Transcribing agency FEU-NRMF MEDICAL LIBRARY
041 ## - LANGUAGE CODE
Language code of text/sound track or separate title English
050 ## - LIBRARY OF CONGRESS CALL NUMBER
Classification number RESRAD20150002
245 ## - TITLE STATEMENT
Title The Air within A Case Report : Lymphangioleiomyomatosis
260 ## - PUBLICATION, DISTRIBUTION, ETC. (IMPRINT)
Place of publication, distribution, etc. QUEZON CITY
Name of publisher, distributor, etc. FEU-NRMF
Date of publication, distribution, etc. 2015
300 ## - PHYSICAL DESCRIPTION
Extent 23 PAGES
520 ## - SUMMARY, ETC.
Summary, etc. ABSTRACT: Lymphangiomyomatosis (LAM) is a multi-systemic, rare, progressive and life threatening cystic lung disease that is predominantly sporadic and effects women of childbearing age. It is usually characterized by proliferation of atypical smooth muscle cells around lymphatics, venules and bronchioles. Generally, patient would present with respiratory symptoms varying from simple cough, chest pain, and dyspnea to recurrent pneumothorax as well as pleural effusion. Pneumothorax is almost always present in 50% of the case. Early stages may show normal findings radiographically, but this may progress from retriculo-nodular to cystic of the lung. LAM can often be confused with other disease entities such as bronchiectasis, emphysema, pulmonary Langerhan`s cell histiocytosis (LCH), lymphocytic interstitial pneumonitis and Birt Hogg Dube syndrome (BHD). Because of the similarities of the early signs and symptoms of LAM to other cystic lung disease, diagnostics such as radiography, computed tomography and pulmonary function test are commonly requested to aid in the diagnosis of LAM. This is a case of a 46-year old female who presented with difficulty of breathing and recurrent pneumothorax. Chest radiograph was done revealing repeated collapse of lungs. Likewise chest CT scan showed findings suggestive of Lymphangioleiomyomatosis. However, histopatologic tissue characterization (lung biopsy) remains the definite examination for the diagnosis of this rare disease, which in our patient revealed emphysematous changes with bronchiolectasis. Pulmonary lymphangioleiomyomatosis is progressive and worsens over time. Currently, there has been no cure available to stop the growth and progression of the cysts in LAM. Treatment goal is to ease symptoms and prevent further complication usually by giving medications to improve air flow of lungs, oxygen therapy, remove fluids through chest tubes and aspirations and lung transplantation for severe LAM. There are clinical trials and researches being done to discover and test new treatments for LAM.
521 ## - TARGET AUDIENCE NOTE
Target audience note Research
700 ## - ADDED ENTRY--PERSONAL NAME
Personal name Limpalan Tammang, Jovayna., M.D.
887 ## - NON-MARC INFORMATION FIELD
Content of non-MARC field RC RC 0019
942 ## - ADDED ENTRY ELEMENTS (KOHA)
Source of classification or shelving scheme Library of Congress Classification
Koha item type Research
Holdings
Withdrawn status Lost status Source of classification or shelving scheme Damaged status Not for loan Home library Current library Shelving location Date acquired Total Checkouts Full call number Barcode Date last seen Price effective from Koha item type
    Library of Congress Classification     Far Eastern University - Nicanor Reyes Medical Foundation Far Eastern University - Nicanor Reyes Medical Foundation Research 01/18/2016   RAD20150002 R000465 03/01/2016 07/22/2016 Research